Ohrmuschelfehlbildung
Microtia •
Microtia - Ganzer Fall bei Radiopaedia
Microtia •
Microtia: grade III - Ganzer Fall bei Radiopaedia
Microtia •
External auditory canal atresia - Ganzer Fall bei Radiopaedia
Fetal
hydrocephalus • Craniofacial malformations (antenatal ultrasound) - Ganzer Fall bei Radiopaedia
Microtia refers to a small pinna of the ear, when is it completely absent it is termed anotia.
Epidemiology
The estimated incidence at around 1:9000 live births. It is more common in males and there is a recognized right sided predilection.
Pathology
Associations
Microtia can be associated with a wide spectrum of inner and middle ear anomalies . Isolated microtia is relatively uncommon. The most frequent associations include:
- ossicular dysplasia
- external auditory canal stenosis
- external auditory canal atresia
Wider organ associations include:
- renal anomalies
Syndromic associations include:
Classification
It is classified into four grades based on increasing severity:
- grade I: slightly small ear with identifiable structures; external auditory canal small but present
- grade II: partial or hemiear with a occluded or stenotic external ear canal producing a conductive hearing loss
- grade III: absence of the external ear with a small peanut like vestige structure and an absence of the external ear canal and eardrum
- grade IV: complete absence (anotia)
Siehe auch:
- Down-Syndrom
- einseitige Nierenagenesie
- Franceschetti-Zwahlen-Syndrom
- Goldenhar-Gorlin-Syndrom
- Gehörgangsatresie
- Jacobsen syndrome
- OFM Nager-Syndrom
- cross-fused ectopia
und weiter:
Assoziationen und Differentialdiagnosen zu Ohrmuschelfehlbildung: