Staphylom

nicht verwechseln mit: Kolobom

Staphyloma is the term given to an eye whose scleral-uveal coats are stretched with uveal protrusion. This most commonly occurs posteriorly, although anterior staphyloma also is recognized. As opposed to coloboma, staphyloma defect is located off-center from the optic disc, typically temporal to the disc .

Clinical presentation

Patients often present with severe axial myopia.

Pathology

It is an acquired defect secondary to weakness and thinning of the scleral-uveal coats.

Posterior staphyloma
  • progressive myopia (or mega myope) is the most common cause
  • glaucoma
  • scleritis
  • necrotizing infection
  • surgery/trauma
  • radiotherapy
Anterior staphyloma

Seen secondary to inflammation or infection of the sclero-corneal lining of the eye.

Radiographic features

  • increased eye size
  • focal deformity (not as marked as coloboma), usually posterior
  • non-enhancing uveo-sclera

Differential diagnosis

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