J-förmige Sella turcica
Macrocephaly
• Mucopolysaccharidoses - Ganzer Fall bei Radiopaedia
J-shaped
sella • Mucopolyssaccharidosis - Ganzer Fall bei Radiopaedia
J-shaped
sella • J shaped sella and simple pituitary cyst - Ganzer Fall bei Radiopaedia
J-shaped
sella • Achondroplasia - Ganzer Fall bei Radiopaedia
A J-shaped sella is a variant morphology of the sella turcica, whereby the tuberculum sellae is flattened, thus forming the straight edge of the "J". The dorsum sellae remains rounded and forms the loop of the "J".
Differential diagnosis
Differential diagnosis for a J-shaped sella includes :
- anatomic variant (~5% of children)
- optic chiasm glioma
- hydrocephalus: mild
- mucopolysaccharidoses: e.g. Hurler syndrome
- achondroplasia
- neurofibromatosis
- pituitary mass (rare)
Mnemonics
CONMAN
- C: chronic hydrocephalus
- O: optic chiasm glioma, osteogenesis imperfecta
- N: neurofibromatosis
- M: mucopolysaccharidoses
- A: achondroplasia
- N: normal variant
MAN PHON
- M: mucopolysaccharidoses
- A: achondroplasia
- N: neurofibromatosis
- P: pituitary mass
- H: hydrocephalus
- O: optic chiasm glioma
- N: normal variant
Siehe auch:
- Hydrocephalus
- Achondroplasie
- Mukopolysaccharidose
- Mukopolysaccharidose Typ I-H
- kongenitale Anomalien der Sellaregion
und weiter:
Assoziationen und Differentialdiagnosen zu J-förmige Sella turcica:
