Gorlin-Goltz-Syndrom

Masses of
developmental and genetic origin affecting the paediatric craniofacial skeleton. Typical manifestations of nevoid basal cell carcinoma syndrome (NBCCS) in a 16-year-old boy. a Orthopantomography (OPT) shows cystic lesions of the mandible and maxilla (arrows), with unilocular and multilocular pattern and smooth or scalloped borders associated with displaced and unerupted permanent teeth. b Coronal CT scan (bone window) shows ectopic calcifications of the falx cerebri and tentorium cerebelli (arrows) and spotted meningeal calcifications (arrowheads). Brain MRI reveals a cavum veli interpositi on axial T2 (asterisk in c) and coronal contrast-enhanced T1 (asterisk in d) and also vermian dysgenesis (arrowheads in d)

Gorlin-Goltz
syndrome • Gorlin-Goltz syndrome - Ganzer Fall bei Radiopaedia

Gorlin-Goltz
syndrome • Gorlin syndrome - Ganzer Fall bei Radiopaedia

Gorlin-Goltz
syndrome • Gorlin-Goltz syndrome - Ganzer Fall bei Radiopaedia

Gorlin-Goltz
syndrome • Gorlin-Goltz syndrome - incidental posterior communicating aneurysm - Ganzer Fall bei Radiopaedia

Gorlin-Goltz
syndrome • Odontogenic keratocysts - Ganzer Fall bei Radiopaedia

Gorlin-Goltz
syndrome • Gorlin-Goltz syndrome - Ganzer Fall bei Radiopaedia

Gorlin-Goltz-Syndrom
Basalzellkarzinome in Kombination mit multiplen Kieferzysten und RippenanomalienSiehe auch:
- Balkenagenesie
- Pectus excavatum
- hemivertebrae
- Gabelrippe
- Hypertelorismus
- Pectus carinatum
- Syndaktylie
- Medulloblastom
- frontal bossing
- lytische Unterkieferläsionen
- Lippen-Kiefer-Gaumen-Spalte
- Kolobom
- Mikrophthalmus
- Unterkieferläsionen
- Cherubismus
- Keratozystischer odontogener Tumor
- Makrozephalie
- Fibrom des Ovars
- kardiales Fibrom
- Phakomatosen
- Trichoepitheliom
- shortened 4th metacarpal bones
und weiter:
- angeborene Wirbelanomalien
- orbital hypertelorism
- Café-au-lait-Fleck
- subkutane Verkalkungen
- conditions involving skin and bone
- Goltz-Gorlin-Syndrom
- diffuse dural calcification
- Zyste Maxilla
- keratocystic odentogenic tumour
- short metacarpals (mnemonic)
- keratocyst
- Basaliom
- osteogenic jaw cyst
- Greig-Syndrom
- Verkürzung Metakarpale vier oder fünf
