Jaffe-Campanacci syndrome
Jaffe-Campanacci-Syndrome,
boy 7 Y, tibial bowing and cortical/subcortial mixed sclerosis
Osteofibrous
dysplasia-like adamantinoma treated via intercalary segmental resection with partial cortex preservation using pedicled vascularized fibula graft: a case report. The X-ray, CT image, and MR images of the tumor. a Anteroposterior radiograph. b Lateral radiograph. c Axial CT image. d T1-weighted magnetic resonance sagittal image. e T2-weighted magnetic resonance sagittal image
Osteofibrous
dysplasia-like adamantinoma treated via intercalary segmental resection with partial cortex preservation using pedicled vascularized fibula graft: a case report. The mass was a heterogeneously hypointense and isointense on a T1-weighted magnetic resonance image and b heterogeneously hyperintense on short TI inversion recovery magnetic resonance image. No pathological fracture was confirmed
Osteofibrous
dysplasia • Osteofibrous dysplasia of the tibia - Ganzer Fall bei Radiopaedia
Osteofibrous
dysplasia • Osteofibrous dysplasia of the tibia - Ganzer Fall bei Radiopaedia
Osteofibrous
dysplasia • Osteofibrous dysplasia - tibia - Ganzer Fall bei Radiopaedia
Osteofibrous
dysplasia • Osteofibrous dysplasia - Ganzer Fall bei Radiopaedia
Jaffe-Campanacci syndrome is characterized by:
- multiple non-ossifying fibromas of the long bones and jaw
- café au lait spots
- intellectual disability
- kyphoscoliosis
- hypogonadism or cryptorchidism
- ocular malformations
- cardiovascular malformations
- giant cell granuloma of the jaw
History and etymology
It is named after Mario Campanacci, Italian physician (1932-1999), and Henry Lewis Jaffe, American pathologist (1896-1979) .
Differential diagnosis
Consider:
Siehe auch:
- nicht ossifizierendes Fibrom
- Fibröse Dysplasie
- Osteoid-Osteom
- Kryptorchismus
- Ossifizierendes Fibrom
- Adamantinom der langen Röhrenknochen
- Admantinom mit dem Bild einer osteofibrösen Dysplasie
und weiter:
Assoziationen und Differentialdiagnosen zu Jaffé-Campanacci-Syndrom:
