Duplikationszyste des Ösophagus
Esophageal duplication cysts are a type of congenital foregut duplication cyst.
Epidemiology
Less common compared to other foregut duplication cysts. There may be an increased male predilection .
Clinical presentation
Patients are generally asymptomatic but may complain of dysphagia due to esophageal compression. They typically present in childhood.
Pathology
They are a congenital malformation of the posterior primitive foregut and results from an aberration of the posterior division of the embryonic foregut at 3-4 weeks gestation. They are commonly lined by gastric epithelium. This ectopic gastric mucosa is prone to infection, perforation and hemorrhage.
Location
It mainly occurs in the thoracic esophagusand are more common on the right particularly in the distal esophagus.
Associations
- spina bifida
- esophageal atresia
- other duplication cysts of the gut
Radiographic features
Plain radiograph
Well defined soft tissue density in close association with the esophagus.
Fluoroscopy
On barium swallow, the cyst may cause extrinsic compression of the esophagus.
CT
Well defined thick-walled structure with internal fluid density noted along the esophagus.
MRI
- T1: low to intermediate signal intensity
- T2: high signal intensity
Treatment and prognosis
Surgical resection is the mainstay of management . Prognosis tends to be very good as recurrence is rare .
Complications
Recognized complications include carcinoma arising within the cyst . If gastric mucosa is present, peptic ulceration may occur. Very occasionally they may perforate, hemorrhage or erode into adjacent structures.
Differential diagnosis
For uncomplicated cysts consider:
- congenital cysts and malformations in the region
- pericardial cyst
- cystic hygroma/lymphangioma
- neurenteric cyst
- anterior or lateral meningocele
- thyroid colloid cyst
- thyroglossal duct cyst
- branchial cleft cyst
- thymic cyst
- cervical lymphadenopathy
- esophageal malignancy
- pancreatic pseudocyst: for retroperitoneal bronchogenic cysts or for pancreatic pseudocysts that extend intrathoracically through the aortic or esophageal hiatus
For complicated cysts (e.g. with hemorrhage/necrosis) the differential can be broader and can include:
- abscess(es)
- enlarged lymph nodes (especially centrally necrotic)
- pulmonary masses
- esophageal malignancy
- hematoma
See also
Siehe auch:
- Bronchogene Zyste
- Duplikationszyste des Magens
- Duplikationszysten gastrointestinal
- Duplikationszyste des ösophagogastralen Übergangs
- Ösophagusduplikatur
- Ösophagusduplikatur versus bronchogene Zyste